Palatal Manifestation of Langerhans cell histiocytosis in a 20 month old child: A Rare presentation

Abstract

Background- Langerhans cell histiocytosis (previously known as histiocytosis X) is an inflammatory myeloid neoplasm commonly occurring in bones and skin but can involve other organs also, although it is a rare disease it is fairly common in young children. Most commonly seen in age group 1-3 years old.
Methods – A case of a 20-month-old boy with a chief complaint of growth in the hard palate since 3 months. On intraoral examination ulcerative growth was observed on hard palate extending from right side of 1st premolar to left side of 1st premolar. The ultrasonogram of whole abdomen was done which revealed cystitis. CECT scan of oral cavity was done and which showed ill-defined mildly enhanced soft tissue density mass.
Result – After serial examinations definite diagnosis of Langerhans cell histiocytosis was confirmed and surgical removal of bilateral lower part of the maxilla, teeth and hard palate with the primary lesion was done.
Conclusion-Despite all the major advances in our medical field it is difficult to understand and diagnose LCH. By doing detailed examinations it is possible to narrow down the diagnosis and planning accurate management.